Skull base chordoma mimicking a preauricular neoplasm in a child: Clinicopathological features and biological behaviour

Suba, Zsuzsanna and Hauser, Péter and Garami, Miklós and Martonffy, Katalin and Szabó, György and Szende, Béla and Tarján, Ildikó and Gábris, Katalin and Barabás, József (2007) Skull base chordoma mimicking a preauricular neoplasm in a child: Clinicopathological features and biological behaviour. Journal of Cranio-Maxillofacial Surgery, 35 (1). pp. 35-38. ISSN 1010-5182

PDF 1082220.pdf Restricted to Registered users only Download (677kB) | Request a copy

Abstract

Introduction: The extreme rarity of chordomas in childhood, the slow growing nature of these tumours and the diverse symptoms may cause many diagnostic problems. Patient: A 9-year-old girl presented with an unusual manifestation of a skull base chordoma. The clinical and pathological features were analysed. Result: In the present case, the initial symptoms of the skull base tumour were completely misleading. The otodynia, the masticatory difficulties and the mass in the preauricular region were not characteristic of skull base chordomas. The female sex, the young age, the large tumour size and the atypical histological pattern of the tumour all indicated a very poor prognosis. Conclusion: The rarity of this tumour in childhood and the atypical lateral and intracranial spread resulted in a serious delay of the diagnosis and in a fatal outcome.

Actions (login required)

Edit Item